Intracranial Rosai Dorfman disease – A rare differential diagnosis of multiple meningiomas: a case report

José L. Navarro-Olvera, Department of Neurosurgery, Mexico General Hospital, Mexico City, Mexico
Gustavo Parra-Romero, Department of Neurosurgery, Mexico General Hospital, Mexico City, Mexico
Antonio Cruz-Cruz, Department of Neurosurgery, Mexico General Hospital, Mexico City, Mexico
Erick Gómez-Apo, Department of Neuropathology, Mexico General Hospital, Mexico City, Mexico
Laura Chávez-Macias, Department of Neuropathology, Mexico General Hospital, Mexico City, Mexico
José D. Carrillo-Ruiz, Department of Neurosurgery, Mexico General Hospital; Research Direction, Mexico General Hospital; Faculty of Health Sciences, Anahuac University North Campus. Mexico City, Mexico

Rosai Dorfman Destombes (RDD) disease is a non-Langerhans histiocytosis. The central nervous system is affected in < 5% of cases. We report the case of a 59-year-old man, who began 8 months before admission with headache, diminished visual acuity in the temporal hemifields, hyposmia, and seizures. Magnetic resonance imaging showed three midline skull-base lesions in anterior, media, and posterior fossae. We performed a complete resection of symptomatic lesions using a bifrontal craniotomy. The histopathological analysis determined RDD, therefore, we started steroid treatment. Our case description is due to the diagnosis and location, one of the rarest reported to date in the literature.

Palabras clave: Intracranial. Multiple meningiomas. Rosai Dorfman disease. Sinus histiocytosis.