open access

Vol 2, No 2 (2017)
Case report
Published online: 2017-06-28
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Intravitreal anti-VEGF therapy in macular oedema secondary to racemose haemangiomatosis of the retina

Magdalena Tylus1, Jerzy Mackiewicz1, Joanna Dolar-Szczasny1, Anna Święch-Zubilewicz1
·
Ophthalmol J 2017;2(2):58-60.
Affiliations
  1. Department of Vitreoretinal Surgery, Medical University in Lublin, Lublin, Poland, Poland

open access

Vol 2, No 2 (2017)
CASE REPORTS
Published online: 2017-06-28

Abstract

Racemose haemangiomatosis of the retina is a sporadic, mostly unilateral, congenital arteriovenous malformation (AVM), comprising abnormal junctions between arteries and veins that omit capillaries. Typically, vascular malformations are asymptomatic and incidentally discovered. Advanced changes may be related to the presence of subretinal fluid and exudates, even though these lesions are classified as benign. Many complications can lead to severe or permanent visual impairment. Direct methods of treatment of primary retinal vascular anomalies have not been developed yet. The aim of this case report is to present the anti-VEGF therapy in the treatment macular oedema secondary to racemose haemangioma.

Abstract

Racemose haemangiomatosis of the retina is a sporadic, mostly unilateral, congenital arteriovenous malformation (AVM), comprising abnormal junctions between arteries and veins that omit capillaries. Typically, vascular malformations are asymptomatic and incidentally discovered. Advanced changes may be related to the presence of subretinal fluid and exudates, even though these lesions are classified as benign. Many complications can lead to severe or permanent visual impairment. Direct methods of treatment of primary retinal vascular anomalies have not been developed yet. The aim of this case report is to present the anti-VEGF therapy in the treatment macular oedema secondary to racemose haemangioma.

Get Citation

Keywords

racemose haemangiomatosis, anti-VEGF, macular oedema, intravitreal injection

About this article
Title

Intravitreal anti-VEGF therapy in macular oedema secondary to racemose haemangiomatosis of the retina

Journal

Ophthalmology Journal

Issue

Vol 2, No 2 (2017)

Article type

Case report

Pages

58-60

Published online

2017-06-28

Page views

631

Article views/downloads

1266

DOI

10.5603/OJ.2017.0014

Bibliographic record

Ophthalmol J 2017;2(2):58-60.

Keywords

racemose haemangiomatosis
anti-VEGF
macular oedema
intravitreal injection

Authors

Magdalena Tylus
Jerzy Mackiewicz
Joanna Dolar-Szczasny
Anna Święch-Zubilewicz

References (16)
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