Rare Case of Isolated Dural Marginal Zone Lymphoma

 

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Introduction

Lymphomatous involvement of the central nervous system (CNS) may manifest either as the sole area of disease (i.e., primary CNS lymphoma [PCNSL]) or more commonly as part of a systemic disease.

PCNSL accounts for <1% of all non-Hodgkin’s lymphoma cases and approximately 4% of newly diagnosed primary CNS tumors.[1] Most cases of PCNSL are aggressive, especially in the settings of underlying immunocompromised state.[2] Dural lymphomas (DLs) are a rare subtype of PCNSL that involve the dura mater without infiltration to the brain parenchyma. Low-grade lymphomas, especially marginal zone subtype, constitute majority of DLs. Herein, we report a case of primary dural marginal zone lymphoma (MZL).

Publication History

Received: 08 January 2020

Accepted: 13 February 2020

Article published online:
23 May 2021

© 2020. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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