Improvement of a Compressed Inferior Vena Cava due to IgG4-related Retroperitoneal Fibrosis with Steroid Therapy

Mizuki Nishimura; Terumi Kamisawa; Yasuyuki Kitahara; Akihiro Nishizawa; Taku Tabata; Seiichi Hara; Sawako Kuruma; Kazuro Chiba; Takashi Fujiwara; Go Kuwata; Hideto Egashira; Koichi Koizumi; Junko Fujiwara; Takeo Arakawa; Kumiko Momma

doi:10.2169/internalmedicine.51.7378

CASE REPORTS

Improvement of a Compressed Inferior Vena Cava due to IgG4-related Retroperitoneal Fibrosis with Steroid Therapy

Mizuki Nishimura, Terumi Kamisawa, Yasuyuki Kitahara, Akihiro Nishizawa, Taku Tabata, Seiichi Hara, Sawako Kuruma, Kazuro Chiba, Takashi Fujiwara, Go Kuwata, Hideto Egashira, Koichi Koizumi, Junko Fujiwara, Takeo Arakawa, Kumiko Momma

Author information

Mizuki Nishimura
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Terumi Kamisawa
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Yasuyuki Kitahara
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Akihiro Nishizawa
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Taku Tabata
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Seiichi Hara
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Sawako Kuruma
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Kazuro Chiba
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Takashi Fujiwara
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Go Kuwata
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Hideto Egashira
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Koichi Koizumi
Department of Internal Medicine, Tokyo Metropolitan Komagome Hospital, Japan
Junko Fujiwara
Department of Endoscopy, Tokyo Metropolitan Komagome Hospital, Japan
Takeo Arakawa
Department of Endoscopy, Tokyo Metropolitan Komagome Hospital, Japan
Kumiko Momma
Department of Endoscopy, Tokyo Metropolitan Komagome Hospital, Japan

Keywords: retroperitoneal fibrosis, IgG4, inferior vena cava, steroid

JOURNAL OPEN ACCESS

2012 Volume 51 Issue 13 Pages 1705-1707

DOI https://doi.org/10.2169/internalmedicine.51.7378

Details

Abstract

A 79-year-old man had a 3.5-year history of edema of the lower extremities of unknown etiology. Abdominal computed tomography showed a soft tissue mass around the abdominal aorta, and the biopsy revealed dense fibrosis with abundant infiltration of IgG4-positive plasma cells. His serum IgG4 level was increased to 188 mg/dL. His lower extremity edema was induced by stenosis of the inferior vena cava (IVC) due to the mass. With a diagnosis of IgG4-related retroperitoneal fibrosis, he was treated with steroid, and the leg edema decreased with improvement of patency of the IVC and reduction of the soft tissue mass.

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