Chest
Aberrant Left Pulmonary Artery: Clinical and Embryologic Factors
Section snippets
Case Report
An infant was seen at 2½ months of age with a history of inspiratory and expiratory stridor that had been present since birth. Growth and development were completely within normal limits, as were the findings from physical examination, with the exception of the examination of the cardiorespiratory system. Maximal cardiac sounds were heard loudest over the right side of the chest, and harsh stridulous breathing was noted on both inspiration and expiration. Normal breath sounds were noted
Discussion
The diagnosis of pulmonary arterial sling may be suspected on the basis of clinical symptoms and radiographic findings. Respiratory distress, if present, usually manifests itself during early infancy. Signs of expiratory obstruction may predominate, since compression of the distal airway may occur either where the anomalous vessel courses up and over the right main-stem bronchus or at the point where it passes between the distal trachea and esophagus just above the carina (Fig 1).
Suggestive
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Cited by (42)
Partial anomalous left pulmonary artery in heterotaxy syndrome. A case report and review of literature
2021, Progress in Pediatric CardiologyCitation Excerpt :It has been described in association with normal hearts [9–11], coarctation of the aorta with mitral stenosis [12,13], double outlet right ventricle (DORV), hypoplastic left heart, pulmonary stenosis, subaortic ventricular septal defect VSD, and atrial septal defect [12,14], multiple VSDs, and a PDA [2,3,15], partial AV canal [16], hypoplastic left heart syndrome [7], tetralogy of Fallot [7], and Kabuki syndrome [17–19]. Bamman et al. reported a case of two LPAs- one arising from its expected origin and the second arising from the RPA, circling over right lower bronchus and passing between trachea and esophagus forming a pulmonary artery sling with distal tracheal compression [9]. Koch et al. described a duplicated LPA, associated with coarctation of the aorta, mitral stenosis, and an imperforate anus, which did not form a partial pulmonary artery sling or any effect on the airway [13].
Partial Form of a Pulmonary Artery Sling
2009, Annals of Thoracic SurgeryLeft Pulmonary Artery Sling Complex: Computed Tomography and Hypothesis of Embryogenesis
2007, Annals of Thoracic SurgeryCitation Excerpt :From our data, we presented strong correlation among them. It is believed that the cause of LPA sling is multifactorial [12]. There is evidence of genetic-related factors such as the case report of LPA sling in identical twins [13], and in patients with trisomies 18 [14] and 21 [13, 15].
Noninvasive diagnosis of partial anomalous left pulmonary artery
2001, Journal of the American Society of EchocardiographyPartial anomalous left pulmonary artery: Report of two cases and review of literature
2015, Cardiology in the Young
Manuscript received May 26; revision accepted November 22.