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CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2021; 11(02): 104-106
DOI: 10.1055/s-0040-1722425
Case Report

Cherubism: Report of a Case

Sachin G. Ram
1   Dental Department, Best Hospital, Chennai, Tamil Nadu, India
,
Vidya Ajila
2   Department of Oral Medicine and Radiology, A.B. Shetty Memorial Institute of Dental Sciences, Nitte (Deemed to be University), Mangalore, India
,
Subhas G. Babu
2   Department of Oral Medicine and Radiology, A.B. Shetty Memorial Institute of Dental Sciences, Nitte (Deemed to be University), Mangalore, India
,
Pushparaja Shetty
3   Department of Oral Pathology and Microbiology, A.B. Shetty Memorial Institute of Dental Sciences, Nitte (Deemed to be University), Mangalore, India
,
Shruthi Hegde
2   Department of Oral Medicine and Radiology, A.B. Shetty Memorial Institute of Dental Sciences, Nitte (Deemed to be University), Mangalore, India
,
Devika S. Pillai
4   Dr Rajesh’s Dental Lounge, Oachira, Kollam, Kerala, India
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Abstract

Cherubism, also known as familial fibrous dysplasia of the jaws or familial multilocular cystic disease is a rare hereditary, developmental disorder. This condition affects the posterior region of the jaws bilaterally in children belonging to the age group of 2 to 5 years. Maximum growth is recorded till puberty after which the lesion regresses over a period of time. Cherubism classically manifests radiographically as bilateral, multilocular radiolucencies affecting the posterior mandible and maxilla. Therapeutic management varies from patient to patient and is directed mainly by esthetic and functional concerns. The present report highlights the clinical and radiographic features of nonfamilial cherubism in a 6-year-old girl.

Keywords

cherubism - multilocular - mandible


Publication History

Article published online:
30 December 2020

© 2020. Nitte (Deemed to be University). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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  • References

  • 1 Mani S, Natarajan B, Rajaram K, Sahuthullah YA, Gokulanathan S, Sitra G. Rare form of cherubism: case report with review of literature. J Pharm Bioallied Sci 2013; (Suppl. 02) S142-S146
    CrossrefPubMedGoogle Scholar
  • 2 Papadaki ME, Lietman SA, Levine MA, Olsen BR, Kaban LB, Reichenberger EJ. Cherubism: best clinical practice. Orphanet J Rare Dis 2012; 7 (Suppl. 01) S6
    CrossrefPubMedGoogle Scholar
  • 3 Mehrotra D, Kesarwani A. Nandlal. Cherubism: case report with review of literature. J Maxillofac Oral Surg 2011; 10 (01) 64-70
    CrossrefPubMedGoogle Scholar
  • 4 Jain V, Sharma R. Radiographic, CT and MRI features of cherubism. Pediatr Radiol 2006; 36 (10) 1099-1104
    CrossrefPubMedGoogle Scholar
  • 5 Lima Gde M, Almeida JD, Cabral LA. Cherubism: clinicoradiographic features and treatment. J Oral Maxillofac Res 2010; 1 (02) e2
    PubMedGoogle Scholar
  • 6 Argyris PP, Gopalakrishnan R, Hu Y, Reichenberger EJ, Koutlas IG. Clinicopathologic and molecular characteristics of familial cherubism with associated odontogenic tumorous proliferations. Head Neck Pathol 2018; 12 (01) 136-144
    CrossrefPubMedGoogle Scholar
  • 7 Ramon Y, Engelberg IS. An unusually extensive case of cherubism. J Oral Maxillofac Surg 1986; 44 (04) 325-328
    CrossrefPubMedGoogle Scholar
  • 8 Davis GB, Sinn DP, Watson SW. Case 43, part II: Cherubism. J Oral Maxillofac Surg 1983; 41 (02) 119-120
    CrossrefPubMedGoogle Scholar
  • 9 Agrawal A, Gupta SK, Saxena P, Kumar P. Non-familial cherubism: clinical and radiological findings. BMJ Case Rep 2014; 2014: bcr2013202031
    CrossrefPubMedGoogle Scholar
  • 10 Elshafey R. Imaging of cherubism: case report and review of the literature. Tanta Med J 2014; 42 (01) 42-45
    CrossrefGoogle Scholar
  • 11 Papadaki ME, Lietman SA, Levine MA, Olsen BR, Kaban LB, Reichenberger EJ. Cherubism: best clinical practice. Orphanet J Rare Dis 2012; 71 (Suppl. 01) S6
    CrossrefPubMedGoogle Scholar
  • 12 Deshmukh R, Joshi S, Deo PN. Nonfamilial cherubism: a case report and review of literature. J Oral Maxillofac Pathol 2017; 21 (01) 181
    CrossrefPubMedGoogle Scholar
  • 13 Kheir MK. Case report of nonfamilial cherubism in a toddler: description of clinic-radiographic features and osseous-dental treatments. Case Rep Med 2016; (09) 1-5 Doi:https://doi.org/10.1155/2016/8795765
    CrossrefGoogle Scholar