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CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2020; 39(02): 125-131
DOI: 10.1055/s-0040-1708890
Update Article | Artigo de Atualização
Thieme Revinter Publicações Ltda Rio de Janeiro, Brazil

Management of Chiari I deformity in Children and Adolescents: A report from the Consensus Taskforce of the Brazilian Society of Pediatric Neurosurgery

Avaliação e manejo da deformidade de Chiari I em crianças e adolescentes: Recomendações e resultados da Reunião de Consenso sobre Controvérsias da Sociedade Brasileira de Neurocirurgia Pediátrica
Marcelo Volpon Santos 
1   Division of Pediatric Neurosurgery, Department of Surgery and Anatomy, University of São Paulo, Ribeirão Preto Medical School, Ribeirão Preto, SP, Brazil
,
Luciano Lopes Furlanetti 
2   Department of Neurosurgery, King's College Hospital NHS Foundation Trust, London, United Kingdom
,
Alexandre Casagrande Canheu
3   Division of Pediatric Neurosurgery, Universidade Estadual de Londrina, Londrina PR, Brazil
,
Antonio Rosa Bellas
4   Division of Pediatric Neurosurgery, Fernandes Figueira Hospital – Fundação Oswaldo Cruz, Rio de Janeiro, RJ, Brazil
,
Marcia Cristina da Silva 
5   Department of Neurosurgery, João XXIII Hospital, Belo Horizonte, MG, Brazil
,
Sergio Cavalheiro 
6   Department of Neurosurgery, Federal University of São Paulo, São Paulo, SP, Brazil
,
Ricardo Santos de Oliveira 
7   Division of Neurosurgery, Department of Surgery and Anatomy, Ribeirão Preto Medical School, University of São Paulo, Ribeirão Preto, SP, Brazil
› Author Affiliations
Further Information

Publication History

19 December 2019

15 January 2020

Publication Date:
24 April 2020 (online)

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Abstract

Much controversy remains on the current management of Chiari I deformity (CID) in children, with many clinical, surgical and ethic-legal implications. The Brazilian Society of Pediatric Neurosurgery (SBNPed, in the Portuguese acronym) has put together a panel of experts to analyze updated published data on the medical literature about this matter and come up with several recommendations for pediatric neurosurgeons and allied health professionals when dealing with CID. Their conclusions are reported herein, along with the respective scientific background.

Resumo

Atualmente, ainda persiste muita controvérsia sobre o manejo da deformidade de Chiari I (CID) em crianças, com diversas implicações clínicas, cirúrgicas e ético-legais. Desta forma, a Sociedade Brasileira de Neurocirurgia Pediátrica (SBNPed) reuniu um painel de especialistas para analisar dados atualizados publicados na literatura médica sobre essa entidade clínica e formulou uma série de recomendações, a fim de padronizar as condutas e auxiliar a tomada de decisões clínicas de neurocirurgiões pediátricos e demais profissionais de saúde que tratam de crianças com CID. Suas conclusões são relatadas aqui, juntamente com o respectivo respaldo científico.

Keywords

chiari I deformity - craniocervical junction - filum terminale - guidelines - hindbrain hernia - tonsillar ectopia

Palavras-chave

deformidade de Chiari I - diretrizes - ectopia - herniação tonsilar - phyllo terminal - junção craniocervical
 

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