Download PDF
Int Arch Otorhinolaryngol 2015; 19(03): 266-268
DOI: 10.1055/s-0034-1387164
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Wegener Granulomatosis: Otologic Manifestation as First Symptom

Carla Fabiane da Costa
1   Department of Otorhinolaryngology, Hospital Universitario Evangelico de Curitiba, Curitiba, PR, Brazil
,
Jose Fernando Polanski
1   Department of Otorhinolaryngology, Hospital Universitario Evangelico de Curitiba, Curitiba, PR, Brazil
› Author Affiliations
Further Information

Publication History

09 May 2014

01 July 2014

Publication Date:
11 November 2014 (online)

   Permissions and Reprints

Abstract

Introduction Wegener granulomatosis is a systemic vasculitis affecting small and medium-sized vessels of the upper and lower respiratory tract and kidneys.

Objective To describe a case of Wegener disease with atypical manifestation.

Resumed Report We describe the case of a 50-year-old woman with chronic otitis media and sensorineural hearing loss as the primary symptoms, without other manifestations.

Conclusion In cases of acute ear manifestations with or without hearing loss and with poor response to usual treatments, Wegener granulomatosis should be included among the possible etiologies. After adequate diagnoses and treatment of this rare disease, there was favorable evolution.

Keywords

Wegener granulomatosis - otitis media - hearing loss
 

  • References

  • 1 Rossini BAA, Bogaz EA, Yonamine FK, Testa JRG, Penido NdeO. Refractory otitis media as the first manifestation of Wegener's granulomatosis. Braz J Otorhinolaryngol 2010; 76 (4) 541
    CrossrefGoogle Scholar
  • 2 Scalcon MRR, Pereira IA, Rachid Filho A, Paiva ES. Manifestação otológica localizada em paciente com granulomatose de Wegener. Rev Bras Reumatol 2008; 48 (4) 253-255
    Google Scholar
  • 3 Antunes T, Barbas CSV. Granulomatose de Wegener. J Bras Pneumol 2005; 31 (Suppl. 01) S21-S26
    Google Scholar
  • 4 Pires APBA, Sousa NJA, Sousa RCA , et al. Wegener's granulomatosis presenting with bilateral facial nerve palsy. Acta ORL 2008; 26 (4) 209-259
    Google Scholar
  • 5 Rezende CEB, Rodrigues REC, Yoshimura R, Uvo IP, Rapoport PB. Wegener's granulomatosis: a case report. Rev Bras Otorrinolaringol 2003; 69: 261-265
    CrossrefGoogle Scholar
  • 6 Cahali S, Souza MMA, Silveira MC, Cabali MB, Cahali RB. Wegener's granulomatosis—case report with otological manifestation as first symptom. Braz J Otorhinolaryngol 1997; 63 (1) 72-74
    Google Scholar
  • 7 Takagi D, Nakamaru Y, Maguchi S, Furuta Y, Fukuda S. Otologic manifestations of Wegener's granulomatosis. Laryngoscope 2002; 112 (9) 1684-1690
    CrossrefGoogle Scholar
  • 8 Fauci AS, Haynes BF, Katz P, Wolff SM. Wegener's granulomatosis: prospective clinical and therapeutic experience with 85 patients for 21 years. Ann Intern Med 1983; 98 (1) 76-85
    CrossrefGoogle Scholar
  • 9 Cordier JF, Valeyre D, Guillevin L, Loire R, Brechot JM. Pulmonary Wegener's granulomatosis. A clinical and imaging study of 77 cases. Chest 1990; 97 (4) 906-912
    CrossrefGoogle Scholar
  • 10 Correa JC, Azevedo AG, Rubens J, Rocha G. Granulomatose de Wegener: análise de dois casos. J Bras Med 1985; 48 (6) 34-38
    Google Scholar