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A case of nasal glioma and neurofibromatosis A new association

Published online by Cambridge University Press:  29 June 2007

K. Pollard*
Affiliation:
Senior Registrar in Histopathology, University of Leeds.
D. A. Carter
Affiliation:
Consultant in ENT Surgery, Hull Royal Infirmary.
*
Dr. K. Pollard, Department of Pathology, University of Leeds, Leeds LS2 9JT, Yorkshire, England.

Abstract

A man of 25 with von Recklinghausen's neurofibromatosis (VR) developed nasal polyps. Subarachnoid haemorrhage occurred shortly after surgical excision and he died 9 weeks later. Post-mortem examination showed chronic hydrocephalus due to aqueduct stenosis. Histologically the polyps were a nasal glioma, a forme fruste of anterior encephalocoele not previously associated with VR, though other cranial defects are well recognized. Nasal glioma should be considered in the differential diagnosis of nasal lesions in VR.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1987

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