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Abnormal origin of the left pulmonary artery from the descending aorta and heterotaxy syndrome: an undescribed phenotypic association

Part of: Cardiac Morphology

Published online by Cambridge University Press:  04 June 2021

Anne Moreau de Bellaing Open the ORCID record for Anne Moreau de Bellaing [Opens in a new window] ,
Damien Bonnet  and
Lucile Houyel
Anne Moreau de Bellaing*
Affiliation:
M3C-Necker, Hôpital Necker-Enfants Malades, AP-HP, Paris, France Department of Pediatric Cardiology, Université de Paris, Paris, France
Damien Bonnet
Affiliation:
M3C-Necker, Hôpital Necker-Enfants Malades, AP-HP, Paris, France Department of Pediatric Cardiology, Université de Paris, Paris, France
Lucile Houyel
Affiliation:
M3C-Necker, Hôpital Necker-Enfants Malades, AP-HP, Paris, France Department of Pediatric Cardiology, Université de Paris, Paris, France
*
Author for correspondence: Anne Moreau de Bellaing, MD, PhD, M3C-Necker, Necker-Enfants Malades, 149 rue de Sèvres, Paris 75015, France. Tel: +33(0)613471532; Fax: +33(0)144494340. E-mail: annemdb@aol.com
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Abstract

Extensive screening in a newborn with prenatal suspicion of VACTERL syndrome identified an anomalous origin of the left pulmonary artery from the descending aorta with an arterial duct and left aortic arch, and normal intra-cardiac anatomy. Other anatomical anomalies suggested heterotaxy syndrome. At one-month-old, re-implantation of the 3.5 mm left pulmonary artery was performed by direct tension-low anastomosis. Post-operative course was complicated by severe left pulmonary atelectasis, and the patient died 20 days later.

Keywords

CHDheterotaxy syndromeanomalous left pulmonary arterydescending aortavascular surgery
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 7 , July 2021 , pp. 1193 - 1196
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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