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Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler

Published online by Cambridge University Press:  06 March 2017

Ziyad M. Binsalamah ,
Luis E. De León  and
Jeffrey S. Heinle
Ziyad M. Binsalamah*
Affiliation:
Division of Congenital Heart Surgery, Texas Children’s Hospital, Houston, TX, United States of America Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX, United States of America
Luis E. De León
Affiliation:
Division of Congenital Heart Surgery, Texas Children’s Hospital, Houston, TX, United States of America Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX, United States of America
Jeffrey S. Heinle
Affiliation:
Division of Congenital Heart Surgery, Texas Children’s Hospital, Houston, TX, United States of America Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX, United States of America
*
Correspondence to: Z. M. Binsalamah, MD, MSc, Division of Congenital Heart Surgery, Texas Children’s Hospital; Michael E. DeBakey Department of Surgery, Baylor College of Medicine, 6621 Fannin St, MC19345H, Houston, TX 77030, United States of America. Tel: +1 832 826 1929; Fax: +1 832 825 1905; E-mail: zmbinsal@texaschildrens.org
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Abstract

Cor triatriatum sinister is a very rare cardiac anomaly that may lead to pulmonary hypertension, right ventricular dilation, and eventually right heart failure. We report a case of a toddler who presented with respiratory distress and cardiomegaly and was found to have cor triatriatum sinister with a restrictive communication, decompressing vertical vein, pulmonary hypertension, severe tricuspid regurgitation, and severe right ventricular dysfunction. She underwent a successful surgical repair, with normalisation of right ventricular function and pulmonary artery pressure.

Keywords

Cor triatriatumdecompressing vertical veintricuspid regurgitationintact interatrial septumpersistent levoatrial cardinal vein
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 6 , August 2017 , pp. 1221 - 1224
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Copyright
© Cambridge University Press 2017 

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References

1. Van Praagh, R, Corsini, I. Cor triatriatum: pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and a study of normal development of the pulmonary vein and atrial septum in 83 human embryos. Am Heart J 1969; 78: 379–405.Google Scholar
2. Rodefeld MD, Brown JW, Heimansohn DA, et al. Cor triatriatum: clinical presentation and surgical results in 12 patients. Ann Thorac Surg 1990; 50: 562–568.CrossRefGoogle Scholar
3. Yaroglu Kazanci, S, Emani, S, McElhinney, DB. Outcome after repair of cor triatriatum. Am J Cardiol 2012; 109: 412–416.Google Scholar
4. Lewis FJ, Varco RL, Taufic M, Niazi SA. Direct vision repair of triatrial heart and total anomalous pulmonary venous drainage. Surg Gynecol Obstet 1956; 102: 713–720.Google Scholar
5. Saxena P, Burkhart HM, Schaff HV, Daly R, Joyce LD, Dearani JA. Surgical repair of cor triatriatum sinister: the Mayo Clinic 50-year experience. Ann Thorac Surg 2014; 97: 1659–1663.CrossRefGoogle Scholar
6. Nassar, PN, Hamdan, RH. Cor triatriatum sinistrum: classification and imaging modalities. Eur J Cardiovasc Med 2011; 1: 84–87.Google Scholar
7. Kerkar P, Vora A, Kulkarni H, Narula D, Goyal V, Dalvi B. Percutaneous balloon dilatation of cor triatriatum sinister. Am Heart J 1996; 132: 888–891.CrossRefGoogle Scholar
8. Howe MJ, Thomas MP, Agarwal PP, Bach DS, Rubenfire M. Cor triatriatum: a reversible cause of severe pulmonary hypertension. Can J Cardiol 2015; 31: 548 e1-3.Google Scholar
9. Aliter H, Youssef A, Al-Murayeh M, Gallo R. Cor triatriatum with persistent levoatrial cardinal vein late presented as severe mitral stenosis. J Saudi Heart Assoc 2012; 24: 257–259.Google Scholar
10. Feltri C, Crawley C, Peart I, Pozzi M, Corno AF. Late presentation of cor triatriatum with persistent levoatrial cardinal vein. Asian Cardiovasc Thorac Ann 2008; 16: 149–151.Google Scholar