Case RepositoryA Rare Case of Rosai-Dorfman Disease Affecting the Brachial Plexus: A Case Report
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Case Report
A 24-year-old male patient was referred to our department in January 2020 from the department of neurology with complaints of weakness of the right upper limb and the inability to hold objects with the right hand. This was associated with muscle atrophy of his right upper extremity and continuous, dull, aching pain in both upper limbs for the past 4 years. He also reported gradually increasing weakness of his left upper extremity and both lower limbs over the last 6 months. There was also a
Discussion
Rosai-Dorfman disease is a rare entity affecting the lymph nodes and extranodal tissues. Although a well-established entity, the initial diagnosis of the disease remains a challenge owing to the varied systemic presentations. Clinical features such as low-grade fever, normocytic normochromic anemia, elevated erythrocyte sedimentation rate, leukocytosis, and hyperglobulinemia, are all nonspecific findings.6 The diagnosis of RDD is established by the presence of histological alterations in the
References (9)
- et al.
Osseous Rosai-Dorfman disease presenting as a solitary lesion of the distal radius
J Hand Surg Am
(2019) - et al.
Cutaneous Rosai-Dorfman disease of the forearm: case report
J Hand Surg Am
(2008) - et al.
Sinus histiocytosis with massive lymphadenopathy
Arch Pathol
(1969) - et al.
Extranodal Rosai-Dorfman disease: clinicopathologic series of 10 patients with radiologic correlation and review of the literature
Am J Clinical Pathol
(2016)
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