Pictorial review
Cardiovascular imaging
MR imaging of arrhythmogenic right ventricular dysplasia: What the radiologist needs to know

https://doi.org/10.1016/j.diii.2014.07.009Get rights and content
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Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is an inherited heart muscle disease that predominantly affects the right ventricle. Clinical manifestations are related to severe ventricular arrhythmia that may lead to sudden death, mostly in young patients. Magnetic resonance imaging (MRI), included in the new diagnostic criteria since 2010, aims to detect segmental and global wall motion abnormalities, reduced ejection fraction, right ventricular dilatation and right ventricular diastolic/systolic dysfunction. An MRI assessment of the right ventricle is often challenging, partly because the MRI diagnostic criteria have some limitations, and also because it requires a significant learning curve due to the low prevalence of the disease. Therefore, this article aims to review the pathophysiology of the disease, the cardiac MRI protocol, images of the various stages of this affection as well as the differential diagnosis.

Keywords

Arrhythmogenic right ventricular dysplasia
Cardiac MRI
Cardiomyopathy

Abbreviations

ARVD
Arrhythmogenic right ventricular dysplasia
MRI
Magnetic Resonance Imaging
RV
Right ventricle
LV
Left ventricle
ECG
Electrocardiogram

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