Case reportSpontaneous Coronary Artery Dissection in Ehlers-Danlos Syndrome
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Comment
Operative morbidity in patients with EDS-IV remains high. In a 30-year single institution review, a total of 31 patients with EDS-IV were identified; 24 patients developed 132 vascular complications, and 15 such patients underwent 30 operative interventions for vascular complications. No patient developed a coronary artery aneurysm or dissection [1]. We describe a case of spontaneous LAD coronary artery dissection treated with coronary artery bypass graft. Ehlers-Danlos syndrome is a
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Cited by (29)
French National registry of spontaneous coronary artery dissections : ‘’DISCO registry’’
2023, Annales de Cardiologie et d'AngeiologieSpontaneous Coronary Artery Rupture in Patients With Ehlers-Danlos Syndrome: Mini Review
2022, Cardiovascular Revascularization MedicineAssociation of TSR1 Variants and Spontaneous Coronary Artery Dissection
2019, Journal of the American College of CardiologyPregnancy-Related Spontaneous Coronary Artery Dissection: A Case Series and Literature Review
2017, Journal of Emergency MedicineCitation Excerpt :Estrogen and progesterone impact arterial wall architecture by altering collagen and the composition of reticular fibers, which weaken the vessel wall tunica media (5,15–17). Connective tissue disorders, diseases not known to have been present in any women in our case series, such as Marfan syndrome, Ehlers-Danlos type IV syndrome, systemic lupus erythematosus, polyarteritis nodosa, hypereosinophilic syndrome, and Kawasaki disease, can increase the risk of P-SCAD (18–23). Other contributing factors include intense exercise, oral contraceptives, cocaine use, variant angina, and fibromuscular dysplasia (24–28).
Imaging of acquired coronary diseases: From children to adults
2016, Diagnostic and Interventional ImagingThe pregnant heart: Cardiac emergencies during pregnancy
2015, American Journal of Emergency MedicineCitation Excerpt :More commonly, the cause of AMI in pregnancy is SCAD, but it may also be caused by coronary embolism, vasospasm, thrombus due to a hypercoagulable state, atherosclerosis, or as a complication of preeclampsia [50]. The cause of SCAD is unclear and seems to be related to an underlying vascular predisposition exacerbated by pregnancy, such as connective tissue disorders and vasospasm [51]. When atherosclerosis is suspected, the normal physiology of pregnancy can exacerbate underlying CAD.