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A Rare Case of Malignant Peripheral Nerve Sheath Tumor of Larynx

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

Malignant peripheral nerve sheath tumors are highly aggressive tumors and they arise either de novo or from preexisting benign schwannoma or neurofibromatosis. Malignant peripheral nerve sheath tumor of the larynx is an extremely rare neoplasm, for which accurate diagnosis is difficult and the therapy is usually delayed. Although wide surgical excision is the mainstay of treatment, radiation therapy also plays an important role in the control and treatment of locally recurrent disease and non resectable cases. Here we are reporting a case of malignant peripheral nerve sheath tumor of the larynx without definite evidences of von Recklinghausen’s disease or preexisting benign peripheral nerve sheath tumor.

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Authors and Affiliations

  1. Department of General Surgery, Aster Malabar Institute of Medical Sciences (MIMS), Govindapuram P.O., Calicut, Kerala, 673016, India

    U. V. Akshay Viswanath

  2. Department of Oncosurgery, Aster Malabar Institute of Medical Sciences (MIMS), Calicut, India

    V. P. Salim & Salahudheen Thottiyen

  3. Department of Pathology, Aster Malabar Institute of Medical Sciences (MIMS), Calicut, India

    M. Lilly

Authors
  1. U. V. Akshay Viswanath
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  2. V. P. Salim
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  3. Salahudheen Thottiyen
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  4. M. Lilly
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All authors were involved in the clinical care of the patient. All authors have read and approved the manuscript.

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Correspondence to U. V. Akshay Viswanath.

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Akshay Viswanath, U.V., Salim, V.P., Thottiyen, S. et al. A Rare Case of Malignant Peripheral Nerve Sheath Tumor of Larynx. Indian J Otolaryngol Head Neck Surg 74 (Suppl 2), 2503–2505 (2022). https://doi.org/10.1007/s12070-020-02234-9

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  • DOI: https://doi.org/10.1007/s12070-020-02234-9

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