Abstract
The most conspicuous element of Gorham’s disease is its radiographic features, wherein massive disappearance of the mandible is observed. We report a case of an adolescent boy with massive osteolysis of the mandible in whom the diagnosis of Gorham’s disease was made. A 14-year-old boy was referred to the Department of Oral and Maxillofacial Surgery, Universiti Kebangsaan Malaysia Medical Centre, Kuala Lumpur, for the management of a massive mandibular deformity. He was diagnosed with a hemangioma-like lesion at 1 year of age. The disease had progressed for an unknown number of years. Plain X-rays and computed tomography images were examined for reconstructive surgery planning. Gorham’s disease is self-limiting, but has catastrophic results. The role of imaging is huge, particularly for reconstructive surgery planning.
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Acknowledgements
We thank Dr. Kew Thean Yean, Department of Radiology, Universiti Kebangsaan Malaysia Medical Centre for his help with the imaging.
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Hui Yuh Soh, Azizah Ahmad, Abd Jabar Nazimi, and Roszalina Ramli declare that they have no conflict of interest.
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All procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1964 and later versions.
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Informed consent was obtained from the patient (now aged above 21 years) for being included in the study.
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Soh, H.Y., Fauzi, A.A., Nazimi, A.J. et al. Gorham’s disease of the mandible: radiological features. Oral Radiol 34, 179–184 (2018). https://doi.org/10.1007/s11282-017-0282-z
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DOI: https://doi.org/10.1007/s11282-017-0282-z