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Congenital tracheal malformations

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Abstract

Congenital malformations of the trachea include a variety of conditions that cause respiratory distress in neonates and infants. A number of anomalies are self-limiting while others are life-threatening and require immediate therapy. The prevalence of congenital airway malformations has been estimated to range between 0.2 and 1 in 10,000 live births. The most frequent congenital tracheal malformations are: tracheomalacia, congenital tracheal stenosis, laryngotracheal cleft and tracheal agenesis. The management of congenital tracheal malformations is complex and requires an individualized approach delivered by a multidiscipilinary team within centralized units with the necessary expertise.

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Author information

Authors and Affiliations

  1. Program Director Pediatric Airway Unit, Mackenna Children’s Hospital, Clínica Las Condes Medical Center, University of Chile, Santiago, Chile

    Patricio Varela

  2. Director Pediatric Airway Unit, Gaslinni Institute, Genoa, Italy

    Michelle Torre

  3. Pediatric Otolaryngology and Head and Neck Surgeon, Hospital de Clínicas de Porto Alegre, Porto Alegre, Brazil

    Claudia Schweiger

  4. National Children’s Research Centre, Our Lady’s Children’s Hospital, Dublin, Ireland

    Hiroki Nakamura

Authors
  1. Patricio Varela
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  2. Michelle Torre
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  3. Claudia Schweiger
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  4. Hiroki Nakamura
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Correspondence to Patricio Varela.

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Varela, P., Torre, M., Schweiger, C. et al. Congenital tracheal malformations. Pediatr Surg Int 34, 701–713 (2018). https://doi.org/10.1007/s00383-018-4291-8

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  • DOI: https://doi.org/10.1007/s00383-018-4291-8

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