Abstract
Serous microcystic adenoma of the pancreas is an uncommon tumor in adults, and reported in pediatric patients only a handful of times. The authors present a case of a 6 month patient with incidental finding of a large cystic mass on the tail of the pancreas during an operation for Hirschsprung’s disease. Final pathology was consistent with serous microcystic adenoma. This is the second case report describing this lesion in an infant, and the first time it has been associated with Hirschsprung’s disease.
This is a preview of subscription content, log in via an institution to check access.
References
Sidden CR, Mortele KJ (2007) Cystic tumors of the pancreas: ultrasound, computed tomography, and magnetic resonance imaging features. Semin Ultrasound CT MRI 28:339–356
Shet NS, Cole BL, Iyer RS (2014) Imaging of pediatric pancreatic neoplasms with radiologic-histopathologic correlation. Pediatr Imaging 202:1337–1348
Amiel J, Sproat-Emison E, Garcia-Barcel M et al (2008) Hirschsprung disease, associated syndromes and genetics: a review. J Med Genet 45:1–14
Tampi C, Mullerpata P, Shah R, Jagannath P, Zimmermann A (2006) Microcystic serous cystadenoma of the pancreas: a report of two cases with one of diffuse presentation. Pancreatology 6:248–253
Agarwal N, Kumar S, Dass J, Arora VK, Rathi V (2009) Diffuse pancreatic serous cystadenoma associated with neuroendocrine carcinoma: a case report and review of literature. J Pancreas (Online) 10(1):55–58
Langrehr JM, Bahra M, Kristiansen G, Neumann HPH, Neumann LM, Plockinger U, Hanninen E (2007) Neuroendocrine tumor of the pancreas and bilateral adrenal pheochromocytomas. A rare manifestation of von Hipple-Lindau disease in childhood. J Pediatr Surg 42:1291–1294
Barral M, Soyer P, Dohan A, Laurent V, Hoeffel C, Fishman EK, Boudiaf M (2014) MRI of cystic pancreatic lesions in adults: an update in current diagnostic features and management. Abdom Imaging 39:48–65
Brunschwig A (1942) Surgery of the pancreatic tumors. MO, Mosby, St. Louis, p 164
Gundersen AE, Janis AF (1969) Pancreatic cystadenoma in childhood. J Pediatr Surg 4:478–481
Montero M, Vazquez JL, Rihuete MA, Corton D, Anton L, Soriano D, Tracchia R (2003) Serous cystadenoma of the pancreas in a child. J Pediatr Surg 38(9):E36
Costa S, Sucesso MB, Ferreira AM, Correia F, Silva A, Estevinho N (2011) Pancreatic serous cystadenoma in a child. Eur J Pediatr Surg 21:266–267
Jenkins JM, Othersen HB (1992) Cystadenoma of the pancreas in a newborn. J Pediatr Surg 27(2):1569
Conflict of interest
The authors have no financial disclosures to report.
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Larson, K., Seifarth, F.G., Plesec, T. et al. Serous microcystic adenoma of the pancreas associated with malrotation and Hirschsprung’s disease in an infant. Pediatr Surg Int 31, 417–419 (2015). https://doi.org/10.1007/s00383-015-3663-6
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00383-015-3663-6