Abstract
The supplementary motor area (SMA) syndrome is characterized by transient weakness and akinesia contralateral to the side of the affected hemisphere. The underlying pathology of the syndrome is not fully understood but is thought to be related to lesions in the SMA, residing principally in the mesial superior frontal gyrus (Broadmann’s area 6c). Although the SMA syndrome a well-characterized clinical entity, we report herein, to our knowledge, the first case of isolated lower extremity SMA syndrome in the literature. This case highlights the importance of considering this rare clinical entity in the context of new or worsening postoperative neurologic deficits. Moreover, early studies did not support somatotopic organization of the SMA as in the primary motor cortex; emerging evidence suggests that delicate somatotopic representation may underlie distinct presentations like that reported in the present case.
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18 January 2020
The original version of this article unfortunately contained an error. The author apologizes for having provided an incorrect name: “Ali Moghadammjou” should be “Ali Moghaddamjou”. Given in this article is the correct author name.
18 January 2020
The original version of this article unfortunately contained an error. The author apologizes for having provided an incorrect name: ���Ali Moghadammjou��� should be ���Ali Moghaddamjou���. Given in this article is the correct author name.
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The original version of this article was revised: The original version of this article unfortunately contained an error. The author apologizes for having provided an incorrect name: “Ali Moghadammjou” should be “Ali Moghaddamjou”. Given in this article is the correct author name.
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Samuel, N., Hanak, B., Ku, J. et al. Postoperative isolated lower extremity supplementary motor area syndrome: case report and review of the literature. Childs Nerv Syst 36, 189–195 (2020). https://doi.org/10.1007/s00381-019-04362-2
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DOI: https://doi.org/10.1007/s00381-019-04362-2