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Klüver–Bucy syndrome after unilateral frontotemporal resection in a child with tuberous sclerosis

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Abstract

Klüver–Bucy syndrome (KBS) is a behavioral phenotype that appears most often after bilateral temporal damage. The main features of KBS are compulsion to examine objects orally, increased sexual activity, placidity, hypermetamorphosis (irresistible impulse to notice and react to everything within sight), visual agnosia, and problems with memory. It is more rarely reported in children than in adults. We present a case of KBS in a 2-year-old boy with tuberous sclerosis complex (TSC) after left frontotemporal resection for refractory epilepsy. This is the first KBS after unilateral temporal resection in a child, although it has already been reported in two adult cases. It also is the first case reported in a TSC patient.

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Authors and Affiliations

  1. Department of Neurology, Massachusetts General Hospital, Boston, USA

    Susana Boronat & Elizabeth Anne Thiele

  2. Department of Psychiatry, Massachusetts General Hospital, Boston, USA

    Peter Newberry

  3. Department of Neuroradiology, Massachusetts General Hospital, Boston, USA

    William Mehan

  4. Department of Neurosurgery, Massachusetts General Hospital, Boston, USA

    Ann-Christine Duhaime

  5. Department of Pediatric Neurology, Vall d’Hebron Hospital, Universitat Autònoma de Barcelona, Barcelona, Spain

    Susana Boronat

  6. Pediatric Epilepsy Program, Massachusetts General Hospital, 175 Cambridge Street, Suite 340, Boston, MA, 02114, USA

    Susana Boronat

Authors
  1. Susana Boronat
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  2. Peter Newberry
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  3. William Mehan
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  4. Elizabeth Anne Thiele
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  5. Ann-Christine Duhaime
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Correspondence to Susana Boronat.

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Boronat, S., Newberry, P., Mehan, W. et al. Klüver–Bucy syndrome after unilateral frontotemporal resection in a child with tuberous sclerosis. Childs Nerv Syst 29, 1391–1394 (2013). https://doi.org/10.1007/s00381-013-2127-3

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  • DOI: https://doi.org/10.1007/s00381-013-2127-3

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