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Intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism in a patient with Behçet's disease: a case report and literature review

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Abstract

A 26-year-old woman with intermittent fever was admitted to our hospital, and gradually developed facial edema. Examinations including computed tomography, transesophageal echocardiography, digital subtraction angiography, and pulmonary perfusion scintigraphy revealed intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism. Clinical findings and laboratory data led us to make a diagnosis of Behçet's disease. Combination of intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism are rare complications in Behçet's disease. Behçet's disease should be considered in the differential diagnosis of intracardiac mass of the right heart, and early diagnosis and treatment are essential for the management of Behçet's disease especially with large-vessel manifestations. In addition to a case report, we review the literature and report the characteristics of intracardiac thrombus in Behçet's disease.

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Authors and Affiliations

  1. Department of Cardiovascular, Respiratory and Metabolic Medicine, Graduate School of Medicine, Kagoshima University, 8-35-1 Sakuragaoka, Kagoshima, 890-8520, Japan

    Takashi Kajiya, Ryuichiro Anan, Masahiro Kameko, Shinichi Minagoe, Shuichi Hamasaki & Chuwa Tei

  2. Department of Laboratory and Molecular Medicine, Graduate School of Medicine, Kagoshima University, Kagoshima, Japan

    Naoko Mizukami & Ikuro Maruyama

  3. Department of Cardiovascular Surgery, Graduate School of Medicine, Kagoshima University, Kagoshima, Japan

    Ryuzo Sakata

Authors
  1. Takashi Kajiya
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  2. Ryuichiro Anan
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  3. Masahiro Kameko
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  9. Chuwa Tei
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Correspondence to Ryuichiro Anan.

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Kajiya, T., Anan, R., Kameko, M. et al. Intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism in a patient with Behçet's disease: a case report and literature review. Heart Vessels 22, 278–283 (2007). https://doi.org/10.1007/s00380-006-0973-6

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