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Immunoglobulin G4-related systemic disease: mesenteric and peritoneal involvement with radiopathological correlation and differential diagnoses

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Abstract

Since its first introduction in 2003 by Kamisawa et al., IgG4-related disease has gained wide interest in the imaging community, and several manuscripts have been published regarding its imaging features. In addition to initial observations in the pancreaticobiliary system, it is now well known that the disease may involve every organ system in the body. There is not much information in the imaging literature about the involvement of mesentery, omentum, and peritoneum in this disease. This article aims to provide more information about the imaging findings of IgG4-related disease regarding these areas by making radiopathological correlations and discussing the possible differential diagnoses.

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Authors and Affiliations

  1. Department of Radiology, Hacettepe University School of Medicine, 06100, Ankara, Turkey

    Ali Devrim Karaosmanoglu, Omer Onder, Deniz Akata, Mustafa Nasuh Ozmen & Musturay Karcaaltincaba

  2. Department of Pathology, Hacettepe University School of Medicine, 06100, Ankara, Turkey

    Can Berk Leblebici & Cenk Sokmensuer

Authors
  1. Ali Devrim Karaosmanoglu
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  2. Omer Onder
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  3. Can Berk Leblebici
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  4. Cenk Sokmensuer
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  5. Deniz Akata
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  6. Mustafa Nasuh Ozmen
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  7. Musturay Karcaaltincaba
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Contributions

ADK and OO wrote the manuscript. CBL and CS provided pathology images. DA, MNO and MK edited the text. All of the authors read and approved the final manuscript.

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Correspondence to Ali Devrim Karaosmanoglu.

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Karaosmanoglu, A.D., Onder, O., Leblebici, C.B. et al. Immunoglobulin G4-related systemic disease: mesenteric and peritoneal involvement with radiopathological correlation and differential diagnoses. Abdom Radiol 46, 1977–1991 (2021). https://doi.org/10.1007/s00261-021-03037-4

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  • DOI: https://doi.org/10.1007/s00261-021-03037-4

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