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Extraskeletal myxoid chondrosarcoma arising in the femoral vein: a case report

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Abstract

Soft tissue tumors arising in deep veins of the extremities are uncommon, although a few cases of synovial sarcoma or leiomyosarcoma arising in the femoral vein have been documented. However, to the best of our knowledge, an extraskeletal myxoid chondrosarcoma (EMC) arising in the femoral vein has not been reported in the English literature. We report a case of EMC arising in the femoral vein of a 70-year-old man who presented with right leg edema and was diagnosed with a deep venous thrombosis (DVT) by computed tomography (CT). Magnetic resonance imaging (MRI) revealed a mass in the right proximal thigh that was diagnosed as myxomatous sarcoma by aspiration cytology, and anticoagulant therapy was initiated. The mass was surgically resected en bloc, including the femoral vein and surrounding soft tissue, and the femoral artery was preserved. The femoral vein was not reconstructed. The histologic diagnosis was an extraskeletal myxoid chondrosarcoma. The patient received postoperative local radiation treatment, with a total dose of 60 Gy, and is currently doing well with no evidence of local recurrence or metastasis at 8 months after surgery. In summary, this case report shows that EMC can arise in the femoral vein, and that reconstruction of the femoral vein is not always necessary during surgery for soft tissue tumors.

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The authors declare that they have no conflicts of interest.

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Authors and Affiliations

  1. Division of Orthopedic Surgery, Niigata University Graduate School of Medical and Dental Sciences, 757-1 Asahimachi-dori, Niigata, 951-8510, Japan

    Naoki Oike, Akira Ogose & Hiroyuki Kawashima

  2. Division of Pathology, Niigata University Graduate School of Medical and Dental Sciences, 757-1 Asahimachi-dori, Niigata, 951-8510, Japan

    Hajime Umezu

  3. Division of Radiology, Niigata University Graduate School of Medical and Dental Sciences, 757-1 Asahimachi-dori, Niigata, 951-8510, Japan

    Shoichi Inagawa

Authors
  1. Naoki Oike
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  2. Akira Ogose
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  3. Hiroyuki Kawashima
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  4. Hajime Umezu
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  5. Shoichi Inagawa
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Correspondence to Naoki Oike.

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Oike, N., Ogose, A., Kawashima, H. et al. Extraskeletal myxoid chondrosarcoma arising in the femoral vein: a case report. Skeletal Radiol 43, 1465–1469 (2014). https://doi.org/10.1007/s00256-014-1897-3

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  • DOI: https://doi.org/10.1007/s00256-014-1897-3

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