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Haemophilia imaging: a review

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Abstract

Haemophilia disorders are characterised by a blood coagulation anomaly leading to prolonged and excessive bleeding. Imaging provides an essential role in the investigation of both the musculoskeletal and the non-musculoskeletal complications of haemophilia. Our institution is home to a large tertiary referral centre for haemophilia treatment. Using our broad experience, we present a multi-modality pictorial review of the musculoskeletal manifestations of haemophilia, including haemophilic arthropathy, intra-muscular haemorrhage and haemophilic pseudotumour. The main imaging features of haemophilic arthropathy are described, including synovial hypertrophy, haemosiderin deposition, sub-chondral cyst formation and loss of joint space.

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Acknowledgements

Alistair Calder and Tony Jeswani contributed to the sourcing of images for this article.

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Authors and Affiliations

  1. The Royal Free Hospital, Pond Street, London, NW3 2QG, UK

    Jody Maclachlan, Antony Gough-Palmer, Rikin Hargunani, Joanna Farrant & Brian Holloway

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  1. Jody Maclachlan
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  2. Antony Gough-Palmer
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  3. Rikin Hargunani
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Correspondence to Jody Maclachlan.

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Maclachlan, J., Gough-Palmer, A., Hargunani, R. et al. Haemophilia imaging: a review. Skeletal Radiol 38, 949–957 (2009). https://doi.org/10.1007/s00256-008-0586-5

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  • DOI: https://doi.org/10.1007/s00256-008-0586-5

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