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Left Superior Vena Cava Draining to Left Atrium: A Case Report, Review of the Literature, and Classification

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Abstract

Persistent left superior vena cava (PLSVC) draining to the left atrium (LA) is a rare congenital abnormality that is often asymptomatic and found incidentally on imaging. PLSVC is usually described alongside other congenital defects, such as septal defects, tetralogy of fallot, and aortic coarctation. PLSVC to LA with an atrial septal defect is known as Raghib syndrome, but to our knowledge PLSVC to LA without an atrial septal defect or right superior vena cava has not been described in the literature. Here, we report the presentation of a patient with PLSVC-LA without ASD and propose a classification system for this subset of congenital heart defects to help guide clinical and surgical management of these patients.

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Fig. 1

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Abbreviations

PLSVC:

Persistent left superior vena cava

LA:

Left atrium

ASD:

Atrial septal defect

SVC:

Superior vena cava

ECHO:

Echocardiogram

CT:

Computerized tomography

LVEDP:

Left ventricular end diastolic pressure

PAP:

Pulmonary arterial pressure

References

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Funding

The authors have no funding source to disclose.

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Authors and Affiliations

  1. College of Medicine, Medical University of South Carolina, Charleston, SC, USA

    Cora R. Bisbee & Curry Sherard

  2. Section of Pediatric Cardiothoracic Surgery, Department of Surgery, Medical University of South Carolina, 10 McClennan Banks Drive, Charleston, SC, 29425, USA

    Taufiek Konrad Rajab

Authors
  1. Cora R. Bisbee
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  2. Curry Sherard
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  3. Taufiek Konrad Rajab
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Contributions

CB, CS, and TR: wrote and edited the manuscript text. TR: prepared Fig. 1 and Supplemental Figure 1. CB and CS prepared Table 1. All authors reviewed and approved the manuscript.

Corresponding author

Correspondence to Taufiek Konrad Rajab.

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The authors have no conflicts of interest or disclosures to declare.

Ethical Approval

The Institutional Review Board (IRB) at MUSC did not approve this study.

Informed Consent

Patient written consent for the publication of the study was not received as this report does not contain any personal information that could lead to the identification of the patient.

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Bisbee, C.R., Sherard, C. & Rajab, T.K. Left Superior Vena Cava Draining to Left Atrium: A Case Report, Review of the Literature, and Classification. Pediatr Cardiol (2023). https://doi.org/10.1007/s00246-023-03289-5

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  • DOI: https://doi.org/10.1007/s00246-023-03289-5

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