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Idiopathic Ventricular Fibrillation: Look for the Hidden Guilty—A case of aborted cardiac death

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Abstract

We report a unique case of a 6-year-old male child with aborted sudden cardiac death due to ventricular fibrillation. A rare anomalous aortic origin of the right coronary artery was detected and supposed to be the cause of the malignant arrhythmia. Clinical exome sequencing did not reveal any pathogenic variant related to channelopathies nor other known heart-related genes. The patient underwent cardiac surgery and a cardiac defibrillator was implanted for secondary prevention.

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Acknowledgements

We thank Dr Elisa Del Vecchio and Chiara Mizzon for support.

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Authors and Affiliations

  1. Pediatric Cardiology and Arrhythmia/Syncope Units, Bambino Gesù Children’s Hospital, IRCCS, Rome, Italy

    Marianna Cicenia, Pietro Paolo Tamborrino, Massimo Stefano Silvetti, Anwar Baban & Fabrizio Drago

  2. Department of Cardiac Surgery, Bambino Gesù Children’s Hospital, IRCCS, Rome, Italy

    Sonia Albanese & Adriano Carotti

  3. Laboratory of Medical Genetics, Bambino Gesù Children’s Hospital, IRCCS, Rome, Italy

    Maria Gnazzo

  4. Department of Imaging, Bambino Gesù Children’s Hospital, IRCCS, Rome, Italy

    Aurelio Secinaro

  5. Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Children Hospital, Rome, Italy

    Marianna Cicenia

Authors
  1. Marianna Cicenia
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  2. Pietro Paolo Tamborrino
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  3. Massimo Stefano Silvetti
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  4. Sonia Albanese
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  5. Maria Gnazzo
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  6. Anwar Baban
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  7. Adriano Carotti
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  8. Aurelio Secinaro
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  9. Fabrizio Drago
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Correspondence to Marianna Cicenia.

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Cicenia, M., Tamborrino, P.P., Silvetti, M.S. et al. Idiopathic Ventricular Fibrillation: Look for the Hidden Guilty—A case of aborted cardiac death. Pediatr Cardiol 42, 1650–1652 (2021). https://doi.org/10.1007/s00246-021-02700-3

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  • DOI: https://doi.org/10.1007/s00246-021-02700-3

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