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Double-Outlet Right Ventricle With an Intact Ventricular Septum: A Unique Stage 1 Palliation

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Abstract

This report describes a case of double-outlet right ventricle with intact ventricular septum diagnosed in a newborn male. The initial diagnosis was made by echocardiography. The baby underwent a hybrid procedure including pulmonary artery banding and stenting of the patent ductus arteriosus. He subsequently underwent stenting of the atrial communication. The patient was discharged at 55 days of life with the intent to perform palliative repair at a later date.

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Correspondence to Kiran K. Mallula.

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Subcostal long-axis sweep demonstrating a dilated left atrium with a hypertrophied left ventricle. The interatrial septum is tenting to the right with a restrictive foramen ovale (44.1 mb)

Subcostal short-axis sweep demonstrating a dilated left atrium with a crowded right ventricle, with both the aorta and pulmonary artery arising from the right ventricle (32.1 mb)

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Suprasternal view demonstrating the reversal of flow in the arch of the aorta, which also is hypoplastic (2.75 mb)

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Mallula, K.K., Patel, N.D., Hijazi, Z.M. et al. Double-Outlet Right Ventricle With an Intact Ventricular Septum: A Unique Stage 1 Palliation. Pediatr Cardiol 34, 2086–2088 (2013). https://doi.org/10.1007/s00246-013-0741-1

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  • DOI: https://doi.org/10.1007/s00246-013-0741-1

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