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Transpleural Pulmonary-to-Systemic Venous Collaterals in a Case With Obstructed Scimitar Vein

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Abstract

Scimitar syndrome is a rare cause of left-to-right shunting. Surgery is indicated for a pulmonary-to-systemic blood flow ratio greater than 1.5:1 and not infrequently is complicated by postoperative obstruction. This report presents a case of scimitar syndrome and reviews how magnetic resonance imaging (MRI) can be used for initial and follow-up assessment of the syndrome with emphasis on suspected pulmonary venous obstruction. Given the potential high incidence of postoperative occlusion, MRI provides hemodynamic and anatomic information for both initial and follow-up assessment of scimitar syndrome. MRI clearly demonstrated transpleural pulmonary-to-systemic venous collaterals draining the obstructed scimitar vein.

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Correspondence to Shi-Joon Yoo.

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Wong, D.T.H., Grosse-Wortmann, L. & Yoo, SJ. Transpleural Pulmonary-to-Systemic Venous Collaterals in a Case With Obstructed Scimitar Vein. Pediatr Cardiol 31, 1086–1088 (2010). https://doi.org/10.1007/s00246-010-9741-6

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  • DOI: https://doi.org/10.1007/s00246-010-9741-6

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