Abstract
Desmoplastic infantile gangliogliomas (DIG) are rare intracranial tumors occurring during the 1st year of life. They arise invariably in the supratentorial region and have a great size at presentation, commonly involving more than one lobe. They are composed of a solid peripheral component of variable size, which involves the superficial cerebral cortex and the leptomeninges, and a large cystic part. Despite the great size at presentation and occasional mitotic activity in the variable undifferentiated component, this entity constitutes a distinct clinicopathological entity with benign prognosis. We hereby present the MRI and histological findings of two cases of DIG in infants aged 9 and 10 months, respectively.
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Nikas, I., Anagnostara, A., Theophanopoulou, M. et al. Desmoplastic infantile ganglioglioma: MRI and histological findings case report. Neuroradiology 46, 1039–1043 (2004). https://doi.org/10.1007/s00234-004-1283-2
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DOI: https://doi.org/10.1007/s00234-004-1283-2