Abstract
We experienced a case of a 38-year-old woman with a persistent cough, 24 years after repair of absent pulmonary valve syndrome with anomalous origin of the left pulmonary artery. The right pulmonary artery was massively dilated, thus it caused the compression of the bronchi, whitch was thought to result in her respiratory symptom. This dilatation of the right pulmonary artery seemed to have progressed because of the following two reasons. The first is the pulmonary hypertension caused by the late reconstruction of the left pulmonary artery. The second is residual pulmonary stenosis and regurgitation after the initial operation without a pulmonary valve insertion. We performed a reoperation consisting of reconstruction of the right ventricular outflow tract using a valved conduit and plication of the right pulmonary artery. Her postoperative course has been without any complications and satisfactory for the past 2 years.
Similar content being viewed by others
References
Fallot 3: 1073–1082, 1971
Calder AL, Brandt PWT, Barratt-Boyes BG, Neutze JM: Variant of tetralogy of Fallot with absent pulmonary valve leaflets and origin of one pulmonary artery from the ascending aorta. Am J Cardiol 46: 106–116, 1980
Ilbawi MN, Idriss FS, Muster AJ, Wessel HU, Paul MH, DeLeon SY: Tetralogy of Fallot with absent pulmonary valve. should value insertion be part of the intracardiac repair? J Thorac Cardiovasc Surg 81: 906–915, 1981
McCaughan BC, Danielson GK, Driscoll DJ, McGoon DC: Tetralogy of Fallot with absent pulmonary valve. Early and late results of surgical treatment J Thorac Cardiovasc Surg 89: 280–287, 1985
Karl TR, Musumeci F, de Levai M, Pincott JR, Taylor JFN, Stark J: Surgical treatment of absent pulmonary valve syndrome. J Thorac Cardiovasc Surg 91: 590–597, 1986
Presbitero P, Pedretti E, Orzan F, Malara D, Villani M, Ferrazzi P, Crupi G, Parenzan L: Absent pulmonary valve syndrome with associated anomalies of the pulmonary blood supply. Int J Cardiol 6: 587–596, 1984
Everett DS, Adams AP, Martin A: Haemoptysis. A case report with tetralogy of Fallot with absent pulmonary valve leaflets and anomalous origin of left pulmonary artery. Aust Pediatr J 23: 363–364, 1987
Saxena A, Shrivastava S, Sharma S: Anomalous origin of the left pulmonary artery from the ascending aorta in a patient with tetralogy of Fallot and “absent pulmonary valve”. Int J Cardiol 33: 315–317, 1991
Watterson KG, Malm TK, Karl TR, Mee RBB: Absent pulmonary valve syndrome. Operation in infants with airway obstruction. Ann Thorac Surg 54: 1116–1119, 1992
Sreeram N, Smith A, Peart I: Fallot’s tetralogy with absent pulmonary valve and anomalous origin of the left pulmonary artery. Int J Cardiol 42: 175–177, 1993
42: 83–89, 1994
Momma K, Ando M, Takao A: Fetal cardiac morphology of tetralogy of Fallot with absent pulmonary valve in the rat. Circulation 82: 1343–1351, 1990
Emmanouilides GC, Thanopoulos B, Siassi B, Fishbein M: “Agenisis” of ductus arteriosus associated with the syndrome of tetralogy of Fallot and absent pulmonary valve. Am J Cardiol 37: 403–409, 1976
Snir E, de Levai MR, Elliott MJ, Stark J: Current surgical technique to repair Fallot’s tetralogy with absent pulmonary valve syndrome. Ann Thorac Surg 51: 979–982, 1991
41: 57–62, 1993
Rabinovitch M, Grady S, David I, Van Praagh R, Sauer U, Buhlmeyer K, Castaneda AR, Reid L: Compression of intrapulmonary bronchi by abnormally branching pulmonary arteries associated with absent pulmonary valves. Am J Cardiol 50: 804–813, 1982
9: 674–679, 1994
Kirklin JW, Barratt-Boyes BG: Cardiac Surgery (Second Edition), New York, 1993, Churchill Livingstone, p1159–1165
44: 114–115, 1991
11: 667–672, 1995
11: 612–619; 1995
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Chikugo, F., Kitagawa, T., Hori, T. et al. A case of reoperation 24 years after repair of absent pulmonary valve syndrome with anomalous origin of the left pulmonary artery. Jpn J Thorac Caridovasc Surg 46, 1329–1333 (1998). https://doi.org/10.1007/BF03217924
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF03217924