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Pseudomixoma peritoneal tipo adenomucinosis peritoneal diseminada con imágenes radiológicas atípicas

Pseudomyxoma peritonei in disseminated peritoneal adenomucinosis: an atypical radiological presentation

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Abstract

Pseudomyxoma peritonei is an unusual condition that has caused much confusion regarding its aetiology, clinical manifestations, treatment and prognosis. It is characterised by mucinous ascites and diffuse mucinous invasions of the peritoneum. Three histological subtypes have been defined: a) disseminated peritoneal adenomucinosis (peritoneal lesions composed of abundant extra-cellular mucin containing scant simple-to-focally-proliferating mucinous epithelium with little cytological atypia or mitotic activity); b) peritoneal mucinous carcinomatosis (peritoneal lesions composed of more abundant mucinous epithelium with the architectural and cytological features of carcinoma); and c) an intermediate group. The different histological subtypes have different prognoses.

We report a case of disseminated peritoneal adenomatosis, and discuss its clinical management.

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Bibliografía

  1. Sugarbaker PH. Pseudomixoma peritonei. Cancer Treat Res 1996;81:105–19.

    Article  CAS  PubMed  Google Scholar 

  2. Wirtzfeld DA, Rodríguez-Bigas M, Weber T, Petrelli NJ. Disseminated peritoneal adenomucinosis: a critical review. Ann Surg Oncol 1999;6(8):797–801.

    Article  CAS  PubMed  Google Scholar 

  3. Ronnett BM, Zahn CH, Kurman RJ, Kass EM, Sugarbaker PH, Shmookler BM. Disseminated peritoneal adenomucinosis and peritoneal mucinous carcinomatosis. A clinico pathologic analysis of 109 cases with emphasis on distinguishing pathologic features, site of origin, prognosis and relationship to pseudomyxoma peritonei. Anm J Surg Pathol 1995;19:1390–408.

    Article  CAS  Google Scholar 

  4. Sugarbaker PH, Ronnet BM, Archer A, et al.Pseudomixoma peritonei syndrome. Adv Surg 1997;30:233–79.

    Google Scholar 

  5. Sugarbaker PH. Pseudomixoma peritonei: a cancer whose biology is characterized by a redistribution fenomenon. Ann Surg 1994;219:109–11.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  6. Esquivel J, Sugarbaker PH. Clinical presentation of the pseudomyxoma peritonai syndrome. Br J Surg 2000; 87:1414–8.

    Article  CAS  PubMed  Google Scholar 

  7. Jacquet P, Jelinek J, Sugarbaker PH. Use of abdominal computerized tomogram to select peritoneal carcinomatosis patients for the cytoreductive approach. J Am Coll Surg 1995;181:530–8.

    CAS  PubMed  Google Scholar 

  8. Ronnett BM, Yan H, Kurman RJ, Shmookler BM, Wu L, Sugarbaker PH. Patients withpseudomixoma peritonei associated with disseminated peritoneal adenomucinosis have a significantly more favorable prognosis than patients with peritoneal mucinous carcinomatosis. Cancer 2001;92(1):85–92.

    Article  CAS  PubMed  Google Scholar 

  9. Witkamp AJ, De Bree E, Kaag MM, van Slooten GW, Zoetmulder FA.. Extensive surgical cytoreduction and intraoperative hyperthermic intraperitoneal chemotherapy in patients with pseudomyxoma peritonei. Br J Surg 2001;88:458–63.

    Article  CAS  PubMed  Google Scholar 

  10. Carmignani CP, Esquivel J, Sugarbaker PH. Cytoreductive surgery and intraperitoneal chemotherapy for the treatment of peritoneal surface malignancy. Rev Oncol 2003;5(4):192–8.

    Google Scholar 

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Authors and Affiliations

  1. Servicio de Medicina Interna, Hospital Universitario La Fe, Valencia, España

    Manuel Vallalta Morales & Carmen Gil Adiego

  2. Servicio de Oncología Médica, Hospital Universitario La Fe, Avenida Campanar 21, 46009, Valencia, España

    Ángel Segura Huerta, Laura Palomar Abad, Jorge Molina Saera & Roberto Díaz Beveridge

Authors
  1. Manuel Vallalta Morales
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  2. Ángel Segura Huerta
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  3. Carmen Gil Adiego
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  4. Laura Palomar Abad
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  5. Jorge Molina Saera
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  6. Roberto Díaz Beveridge
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Correspondence to Ángel Segura Huerta.

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Morales, M.V., Huerta, Á.S., Adiego, C.G. et al. Pseudomixoma peritoneal tipo adenomucinosis peritoneal diseminada con imágenes radiológicas atípicas. Rev Oncol 6, 173–175 (2004). https://doi.org/10.1007/BF02710120

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  • DOI: https://doi.org/10.1007/BF02710120

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