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Pulmonary emphysema in a neonate with Marfan syndrome

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Abstract

A premature infant with arachnodactyly and congenital cyanotic heart disease had severe pulmonary emphysema, a little-known manifestation of Marfan syndrome. The possible etiologies of emphysema in this syndrome are discussed.

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Authors and Affiliations

  1. Department of Radiology, University of Minnesota Medical School and Hospitals, Minneapolis, Minnesota, USA

    D. L. Day

  2. Department of Laboratory Medicine, University of Minnesota Medical School and Hospitals, Minneapolis, Minnesota, USA

    B. A. Burke

  3. Department of Pathology, University of Minnesota Medical School and Hospitals, Minneapolis, Minnesota, USA

    B. A. Burke

  4. Department of Pediatrics, University of Minnesota Medical School and Hospitals, Minneapolis, Minnesota, USA

    B. A. Burke

Authors
  1. D. L. Day
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  2. B. A. Burke
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Day, D.L., Burke, B.A. Pulmonary emphysema in a neonate with Marfan syndrome. Pediatr Radiol 16, 518–521 (1986). https://doi.org/10.1007/BF02387973

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  • DOI: https://doi.org/10.1007/BF02387973

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