Abstract
After commenting briefly on the literature on Fahr syndrome, we describe a patient with an unusual association of cerebral calcifications and motoneuron disease. We discuss the possible role of brain calcifications in the clinical picture and stress the importance of the routine use of CT scanning and MRI to show further similar associations, possibly leading to a better understanding of the pathophysiology.
Sommario
Dopo brevi considerazioni generali sulla letteratura esistente riguardo la Sindrome di Fahr, gli Autori riportano il caso inusuale di una associazione tra calcificazioni cerebrali massive e motoneuron disease. Vengono quindi discussi i probabili rapporti patogenetici tra le calcificazioni cerebrali e il quadro clinico e rilevata la necessità di ulteriori future segnalazioni riguardo tale associazione, grazie all'uso routinario della TAC e della RMN cerebrale, per una miglior comprensione del problema.
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Eleopra, R., Accurti, I., Neri, W. et al. Unusual case of Fahr syndrome with motoneuron disease. Ital J Neuro Sci 12, 597–600 (1991). https://doi.org/10.1007/BF02336958
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DOI: https://doi.org/10.1007/BF02336958