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Pediatric primary sclerosing cholangitis

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Summary

An 11-year-old male presented with abdominal pain and emesis. Serum chemistries revealed cholestasis and an ERCP demonstrated sclerosing cholangitis. Secondary causes of this disease process were excluded. Sclerosing cholangitis is distinctly uncommon in the pediatric age group, but it should be considered in evaluation of patients of any age with cholestasis. It appears in some cases that there may be subtle histologic and radiographic features which separate the pediatric and adult forms of the disease.

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Authors and Affiliations

  1. Divisions of Gastroenterology, Internal Medicine Departments, Naval Hospital, Portsmouth, Virginia

    David A. Johnson MD,  Edward L. Cattau Jr MD & Joseph E. Hancock MD

  2. Digestive Diseases Division, Department of Medicine, Uniformed Services University of the Health Sciences, 20814, Bethesda, Maryland

    David A. Johnson MD,  Edward L. Cattau Jr MD & Joseph E. Hancock MD

Authors
  1. David A. Johnson MD
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  2. Edward L. Cattau Jr MD
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  3. Joseph E. Hancock MD
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Additional information

The opinions and assertions contained herein are the private ones of the authors and are not to be construed as official or reflecting the views of the Department of Defense, Department of the Navy or the Naval Service at large, or the Uniformed Services University of the Health Sciences.

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Johnson, D.A., Cattau, E.L. & Hancock, J.E. Pediatric primary sclerosing cholangitis. Digest Dis Sci 31, 773–777 (1986). https://doi.org/10.1007/BF01296457

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  • DOI: https://doi.org/10.1007/BF01296457

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