Abstract
An 11-year-old boy with Noonan syndrome presented with shortness of breath secondary to a large spontaneous chylothorax. He was subsequently shown to have pulmonary lymphangiectasia and hypertrophic cardiomyopathy. Dietary management of the chylothorax has successfully relieved his symptoms, although significant effusion persists.
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Fisher, E., Weiss, E.B., Michals, K. et al. Spontaneous chylothorax in Noonan's syndrome. Eur J Pediatr 138, 282–284 (1982). https://doi.org/10.1007/BF00441221
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DOI: https://doi.org/10.1007/BF00441221