Abstract
We describe two patients, brother and sister, with identical pathology, whose only clinical presentation was recurrent massive lower digestive tract bleeding. Haemorrhage was due to a complex form of familial venous vascular malformation in the digestive tract, represented by the existence of varices of colon, small intestine and, to a lesser extent, oesophagus and gastric funcus. We have been able to study, examine and treat both patients for 9 and 3 years respectively.
Résumé
Nous décrivons deux patients frère et sœur avec une pathologie identique qui se résumait à des hémorragies massives récidivantes basses. L'hémorragie était dûe à une forme complexe de malformations veineuses familiales de l'appareil digestif représenté par l'existence de varices du colon, de l'intestin grèle et à un moindre degré de l'œsophage et du fundus gastrique. Nous avons eu la possibilité d'étudier, d'examiner et de traiter ces deux patients respectivement 9 ans et 3 ans.
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Atin, V., Sabas, J.A., Cotano, J.R. et al. Familial varices of the colon and small bowel. Int J Colorect Dis 8, 4–8 (1993). https://doi.org/10.1007/BF00341268
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DOI: https://doi.org/10.1007/BF00341268