Abstract
Biliary atresia (BA) is a progressive cholestatic disease that accounts for nearly 50% of patients referred for liver transplants [1]. Kasai portoenterostomy is the first-line standard treatment for BA and recommended to be performed within 60 days of birth to manage jaundice. However, even if yellowish stool can be eliminated, and a complete correction of the serum bilirubin level to below the normal range can be achieved, then up to half of all BA patients cannot make it through adolescence with their native liver and ultimately require liver transplantation (LT) [2, 3]. Complications of cirrhosis, including portal hypertension, ascites, variceal bleeding, and acute-on-chronic liver failure, are indications for LT [3, 4]. The extrahepatic complications associated with this disease, such as hepatopulmonary syndrome and portopulmonary hypertension, are also indications for LT [4].
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- BA: biliary atresia:
-
LT: liver transplantation
SLT: split liver transplantation
DBD: donation after brain death
DCD: donation after cardiac death
DDLT: deceased donor liver transplantation
IVC: inferior vena cava
LLS: left lateral segment
ERL: extended right lobe
LL: left lobe
RL: right lobe
LDLT: living donor liver transplantation
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Ihara, Y., Mizuta, K. (2021). Operation Procedure: Deceased Donor Liver Transplantation for Biliary Atresia. In: Nio, M. (eds) Introduction to Biliary Atresia. Springer, Singapore. https://doi.org/10.1007/978-981-16-2160-4_25
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DOI: https://doi.org/10.1007/978-981-16-2160-4_25
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