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Desmoid Tumor/Deep-Seated Fibromatosis (Desmoid-Type Fibromatosis)

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Management of Soft Tissue Sarcoma

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Abstract

Desmoids are enigmatic clonal malignancies of myofibroblastic cells that do not have the ability to metastasize, but cause morbidity and occasionally mortality by locally aggressive growth. They are sometimes termed deep fibromatoses, to distinguish them from superficial fibromatoses such as Dupuytren contracture, trigger finger, or Peyronie disease.

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Authors and Affiliations

  1. International Center Department of Surgery, Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Murray F. Brennan MD

  2. Department of Pathology, Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Cristina R. Antonescu MD

  3. Department of Radiation Oncology, Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Kaled M. Alektiar MD

  4. Monter Cancer Center, Hofstra Northwell School of Medicine and Cold Spring Harbor Laboratory, Lake Success, NY, USA

    Robert G. Maki MD, PhD

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  1. Murray F. Brennan MD
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  2. Cristina R. Antonescu MD
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  3. Kaled M. Alektiar MD
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  4. Robert G. Maki MD, PhD
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Brennan, M.F., Antonescu, C.R., Alektiar, K.M., Maki, R.G. (2016). Desmoid Tumor/Deep-Seated Fibromatosis (Desmoid-Type Fibromatosis). In: Management of Soft Tissue Sarcoma. Springer, Cham. https://doi.org/10.1007/978-3-319-41906-0_10

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  • DOI: https://doi.org/10.1007/978-3-319-41906-0_10

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