Abstract
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a highly aggressive tumor of plasmacytoid dendritic cells that commonly presents with involvement of the skin, bone marrow, peripheral blood, and lymph nodes. This diagnosis portends a dismal prognosis. BPDCN has previously been referred to in the literature as blastic NK lymphoma, agranular CD4+ NK-cell leukemia, blastic NK leukemia/lymphoma, and CD4+ CD56+ hematodermic neoplasm, reflecting the initial incorrect belief that the neoplastic cells are derived from NK cells [1].
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Goyal, A., Carter, J.B., Duncan, L.M. (2015). Blastic Plasmacytoid Dendritic Cell Neoplasm. In: Carter, J., Goyal, A., McDivitt Duncan, L. (eds) Atlas of Cutaneous Lymphomas. Springer, Cham. https://doi.org/10.1007/978-3-319-17217-0_21
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