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The ASCRS Textbook of Colon and Rectal Surgery pp 577–586Cite as

Appendiceal Neoplasms

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Abstract

Appendiceal neoplasms are rare. Their incidence ranges between 0.12 and 1.3 per one million population. The diagnosis is frequently made incidentally following appendectomy for presumed appendicitis after histologic review of the resected specimen, occurring in approximately 1% of all appendectomies. A diagnosis of appendiceal adenocarcinoma generally prompts a right hemicolectomy, except when tumor invasion is limited to the submucosa. Low- and high-grade mucinous neoplasms (LAMNs, HAMNs) limited to the appendix can be treated with appendectomy alone. Appendiceal neuroendocrine tumors less than 2 cm in diameter can be treated with appendectomy alone, while incomplete resection, high-risk features, or larger size should prompt consideration of right hemicolectomy.

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Authors and Affiliations

  1. West Florida Healthcare, Department of Surgery, University of Central Florida, Pensacola, FL, USA

    Sanda A. Tan

  2. Mayo Clinic Florida, Department of Surgery, Division of Colorectal Surgery, Jacksonville, FL, USA

    Luca Stocchi

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  1. Sanda A. Tan
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  2. Luca Stocchi
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Correspondence to Luca Stocchi .

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Editors and Affiliations

  1. Department of Colorectal Surgery, Cleveland Clinic, Cleveland, OH, USA

    Scott R. Steele

  2. Department of Colorectal Surgery, Cleveland Clinic, Cleveland, OH, USA

    Tracy L. Hull

  3. University of Chicago Medical Center, Chicago, IL, USA

    Neil Hyman

  4. Department of Surgery, University of Massachusetts Medical School, Worcester, MA, USA

    Justin A. Maykel

  5. Division of Gastrointestinal Surgery, University of Florida, Gainesville, FL, USA

    Thomas E. Read

  6. Department of Colon and Rectal Surgery, Ochsner Clinic, New Orleans, LA, USA

    Charles B. Whitlow

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Tan, S.A., Stocchi, L. (2022). Appendiceal Neoplasms. In: Steele, S.R., Hull, T.L., Hyman, N., Maykel, J.A., Read, T.E., Whitlow, C.B. (eds) The ASCRS Textbook of Colon and Rectal Surgery. Springer, Cham. https://doi.org/10.1007/978-3-030-66049-9_33

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