1 Signs and Symptoms
Orbital LMs generally appear in children in the first few years of life. In a few instances, it is recognized in the teenage years, when the patient presents with abrupt proptosis, ptosis, periocular soft tissue swelling, and ecchymosis resulting from spontaneous or traumatic hemorrhage. LM may also become apparent in adulthood and even in old age. Conjunctival components, such as multiple clear or hemorrhagic cysts, are commonly present and these findings indicate the presence of underlying orbital lesion. These cystic structures are often filled with blood and seen clinically or at the time of surgery and known as chocolate cyst. Patients with orbital LM may have LMs elsewhere in the body, commonly on the palate. Presence of such findings should suggest the orbital diagnosis. The abrupt hemorrhage in the orbit may resolve gradually, but can also recur. The size of the lesions may change with upper respiratory tract infections [1,2,3,4,5,6,7,8,9,10,11].
2 Different...
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Bhattacharjee, K., Medhi, N., Mohapatra, S.S.D. (2021). Lymphatic Malformations. In: Ben Simon, G., Greenberg, G., Prat, D. (eds) Atlas of Orbital Imaging . Springer, Cham. https://doi.org/10.1007/978-3-030-41927-1_105-1
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DOI: https://doi.org/10.1007/978-3-030-41927-1_105-1
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