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Hospital-Based Dermatopathology pp 199–244Cite as

Mucinosis and Disorders of Collagen and Elastic Fibers

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Abstract

Cutaneous mucinoses are a heterogeneous group of disorders having as a common denominator the deposition of an excess of mucin (acid glycosaminoglycans, mostly hyaluronic acid) in the dermis or in the hair follicles. They are divided into primary and secondary forms. Primary cutaneous mucinoses are characterized by specific clinical lesions in which mucin deposition is the distinctive histological sign, while in secondary mucinoses, mucin deposition is simply an accessory histological sign. Disorders of collagen and elastic fibers are divided into hereditary and acquired forms. Both forms can be further divided into those diseases characterized by an increase and those by a decrease in collagen and elastic tissue. A peculiar variant of disorders of dermal connective tissue includes the primary perforating dermatoses.

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Authors and Affiliations

  1. Unit of Dermatology, Department of Medical Sciences and Public Health, University of Cagliari, Cagliari, Sardinia, Italy

    Franco Rongioletti & Caterina Ferreli

  2. Unit of Clinical Dermatology, Department of Dermatology and Cutaneous Surgery, Miller School of Medicine, University of Miami, Miami, FL, USA

    Paolo Romanelli

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  1. Franco Rongioletti
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  2. Paolo Romanelli
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  3. Caterina Ferreli
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Correspondence to Franco Rongioletti .

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Editors and Affiliations

  1. Professor of Pathology, Harvard Medical School, Director of Dermatopathology, Massachusetts General Hospital, Boston, MA, USA

    Mai P. Hoang

  2. Professor of Pathology and Dermatology, Director, Dermatopathology Unit, Duke University Medical Center, Durham, NC, USA

    Maria Angelica Selim

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Rongioletti, F., Romanelli, P., Ferreli, C. (2020). Mucinosis and Disorders of Collagen and Elastic Fibers. In: Hoang, M., Selim, M. (eds) Hospital-Based Dermatopathology. Springer, Cham. https://doi.org/10.1007/978-3-030-35820-4_6

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  • DOI: https://doi.org/10.1007/978-3-030-35820-4_6

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