Nihan Hande Akçakaya1, Mehmet Osman Akçakaya2, Altay Sencer3, Zuhal Yapıcı4

1Istanbul University Aziz Sancar Institute of Experimental Medicine, Department of Genetics, Istanbul, Turkey
2Liv Hospital, Clinic of Neurosurgery, Istanbul, Turkey
3Istanbul University Istanbul Faculty of Medicine, Department of Neurosurgery, Istanbul, Turkey
4Istanbul University Istanbul Faculty of Medicine, Department of Neurology, Istanbul, Turkey

Keywords: Idiopathic intracranial hypertension, pseudotumor cerebri, primary pseudotumor cerebri, optic nerve compartment syndrome, review

Abstract

Idiopathic intracranial hypertension (IIH) is a condition of increased intracranial pressure without a secondary etiology. IIH is seen frequently in young and obese women. Headache, vision problems, and pulsatile tinnitus are the most common symptoms that lead patients to physicians. IIH requires a multidisciplinary approach because it could create permanent morbidity and its treatment plan should be individualized for each patient. The aim of this review was to provide an updated overview of IIH’s pathogenesis, diagnostic criteria, and treatment strategies.