J Korean Soc Spine Surg. 2008 Dec;15(4):286-289. Korean.
Published online Dec 31, 2008.
Copyright © 2008 Korean Society of Spine Surgery
Case Report

The Crowned Dens Syndrome - A Case Report -

Jae-Ryong Cha, M.D., Sung-Do Cho, M.D., Sang-Hun Ko, M.D., Kwang-Hwan Jung, M.D., Yoon-Seok Youm, M.D., Jee-Young Jung, M.D., Ki-Bong Park, M.D. and Chae-Chil Lee, M.D.
    • Department of Orthopedic Surgery, Ulsan University Hospital, Ulsan, Korea.

Abstract

Patients with Crowned dens syndrome typically present with severe neck pain and have calcification around the axial odontoid process on radiographs.

To our knowledge, Crowned dens syndrome is unreported in the Korean literature and the clinical features remain unclear.

We present Crowned dens syndrome as a cause of acute cervical pain and review the literature.

Keywords
Odontoid process; calcification; Crowned dens syndrome

Figures

Fig. 1
(A) Anteroposterior radiographs of the cervical spine showed scoliosis of cervical spine. (B) Lateral radiographs of the cervical spine.

Fig. 2
Patterns of calcifications according to localization and extent in relation to the odontoid process of the axis on computed tomography scans. (A) The axial view of computed tomography scans showed multiple calcifications (0.8×1.2×1.0 cm) in right lateral aspect of odontoid process of C2. (B) The coronal view of computed tomography scans showed calcifications (0.8×1.2×1.0 cm) in right lateral aspect of odontoid process of C2.

Fig. 3
(A,B) Magnetic resonance images of a patient, showing a low-signal intensity change in right lateral aspect of odontoid process of C2.

References

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    1. Malca SA, Roche PH, Pellet W, Combalbert A. Crowned dens syndrome: a manifestation of hydroxyapatite rheumatism. Acta Neurochir (Wien) 1995;135:126–130.
    1. Aouba A, Vuillemin-Bodaghi V, Mutschler C, De Bandt M. Crowned dens syndrome misdiagnosed as polymyalgia rheumatica, giant cell artertitis, meningitis or spondylitis: an analysis of eight cases. Rheumatology 2004;43:1508–1512.
    1. Wu DW, Reginato AJ, Torriani M, Robinson DR, Reginato AM. The crowned dens syndromes as a cause of neck pain: report of two new cases and review of the literature. Arthritis Rheum 2005;53:133–137.
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    1. Sato Y, Yasuda T, Konno S, Kuwayama A, Komatsu K. Pseudogout showing meningoencephalitic symptoms: crowned dens syndrome. Intern Med 2004;43:865–868.

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