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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2016; 26(03): 411-415
DOI: 10.4103/0971-3026.190416
Miscellaneous

Young patient with generalized lymphangiomatosis: Differentiating the differential

Tharani Putta
Department of Radiology, Christian Medical College, Vellore, Tamil Nadu, India
,
Aparna Irodi
Department of Radiology, Christian Medical College, Vellore, Tamil Nadu, India
,
Balamugesh Thangakunam
Department of Pulmonary Medicine, Christian Medical College, Vellore, Tamil Nadu, India
,
Ashwin Oliver
Department of Pulmonary Medicine, Christian Medical College, Vellore, Tamil Nadu, India
,
Rajesh Gunasingam
Department of Radiotherapy, Christian Medical College, Vellore, Tamil Nadu, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

We present the case of a 19-year-old man who was extensively evaluated in multiple centres for long-standing cough, dyspnea, and hemoptysis without a definitive diagnosis. His chest radiograph at presentation showed mediastinal widening, bilateral pleural effusions, and Kerley B lines. Computed tomography of the thorax showed a confluent, fluid-density mediastinal lesion enveloping the mediastinal viscera without any mass effect. There were bilateral pleural effusions, prominent peribronchovascular interstitial thickening, interlobular septal thickening and lobular areas of ground glass density with relative sparing of apices. There were a few dilated retroperitoneal lymphatics and well-defined lytic lesions in the bones. In this case report, we aim to systematically discuss the relevant differentials and arrive at a diagnosis. We also briefly discuss the treatment options and prognosis along with our patient's course in the hospital and final outcome.

Keywords

Cystic mediastinal mass - generalized lymphangiomatosis - pulmonary interstitial thickening - pulmonary lymphangiectasia


Publication History

Article published online:
30 July 2021

© 2016. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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