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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2010; 31(02): 65-68
DOI: 10.4103/0971-5851.71659
CASE REPORT

Giant non-functioning adrenocortical carcinoma: A rare childhood tumor

Viral V Patel
Department of Radiodiagnosis, PramukhSwami Medical College and Shree Krishna Hospital, Karamsad, Gujarat, India
,
Diva S Shah
Department of Radiodiagnosis, PramukhSwami Medical College and Shree Krishna Hospital, Karamsad, Gujarat, India
,
Chandra R Raychaudhari
Department of Radiodiagnosis, PramukhSwami Medical College and Shree Krishna Hospital, Karamsad, Gujarat, India
,
Keyuri B Patel
Department of Radiodiagnosis, PramukhSwami Medical College and Shree Krishna Hospital, Karamsad, Gujarat, India
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Abstract

Adrenocortical carcinoma (ACC) is a rare malignancy, especially in children. The overall incidence is approximately 2 cases per million per year. [1] In children, the incidence is 0.3 cases per million per year, except in southern Brazil where the incidence is 3.4-4.2 cases per million per year. [2] We describe a giant nonfunctioning metastasized ACC in a 6-year-old girl who presented with a history of increasing abdominal girth incidentally noticed by her mother since 1 week. Ultrasound abdomen showed a large right suprarenal tumor with calcifications and necrosis. Empty left renal fossa and compensatory enlarged right kidney were seen. Computed tomography (CT) scan revealed a large heterogenously enhancing right suprarenal mass with calcification and necrosis with pulmonary metastasis. Histopathology report from the right suprarenal mass revealed an ACC. With a stage IV disease, the patient died after 2 months from diagnosis.

Keywords

Adrenocortical carcinoma - adrenocortical tumor - nonfunctioning


Publication History

Article published online:
19 November 2021

© 2010. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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