Korean Circ J. 1991 Jun;21(3):606-613. Korean.
Published online Jun 30, 1991.
https://doi.org/10.4070/kcj.1991.21.3.606
Published online Jun 30, 1991.
https://doi.org/10.4070/kcj.1991.21.3.606
Copyright © 1991 The Korean Society of Circulation
Case Report
Unilateral Pulmonary Vein Atresia with Absent Right Superior Vena Cava
Hyoung Doo Lee, M.D.,
Chung Il Noh, M.D.,
Jung Yun Choi, M.D.
and Yong Soo Yun, M.D.
Abstract
A case of unilateral pulmonary vein atresia with absent right superior vena cava in 9 years-old boy is described with a discussion.
Clinical findings were similar to other reports and consisted of hemoptysis, dyspnea and anemia. A chest X-rary revealed irregular vascular marking on left lung fiedld and increased interstitial marking on right upper lung field.
The diagnosis could be confirmed with radionuclide perfusion study, MRI scan of heart and great vessels and angiography which demonstrated a small right pulmonary artery, pruned its peipheral branches, stasis of contrast material and nonvisualization of draining righ pulmonary veins.
Pneumonectomy, patch angioplasty of diaphargm excision will be necessary.
Keywords
Pulmonary vein atresia; Absent right superior vena cava
Permalink information copied to clipboard