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An Unusual Case of Tricuspid Stenosis
Sara Ferreira
 |
Internal Medicine Department, Centro Hospitalar de São João, Porto, Portugal |
Arsénio Barbosa
|
Internal Medicine Department, Centro Hospitalar de São João, Porto, Portugal |
Filipa Gomes
|
Internal Medicine Department, Centro Hospitalar de São João, Porto, Portugal |
Jorge Almeida
|
Cardiothoracic Surgery Department, Centro Hospitalar de São João, Porto, Portugal |
Jorge Santos Almeida
|
Internal Medicine Department, Centro Hospitalar de São João, Porto, Portugal |
Mário Amorim
|
Cardiothoracic Surgery Department, Centro Hospitalar de São João, Porto, Portugal |
José Paulo Araújo
|
Internal Medicine Department, Centro Hospitalar de São João, Porto, Portugal |
Keywords
Tricuspid stenosis, hypereosinophilic syndrome, Ebstein's anomaly, endomyocardial fibrosis
Abstract
Tricuspid stenosis is an uncommon valvular abnormality commonly associated with other valvular lesions. Ebstein's anomaly is a rare congenital heart malformation characterized primarily by abnormalities of the tricuspid valve and right ventricle. Endomyocardial fibrosis is a restrictive cardiomyopathy observed in tropical and subtropical regions. It may cause right ventricular distortion with apparent apical displacement of the tricuspid valve, mimicking Ebstein’s anomaly. Eosinophilia is the most commonly cited aetiological link in endomyocardial fibrosis. Here we report the case of 42-year-old male patient who presented with heart failure and severe tricuspid stenosis where a diagnosis of hypereosinophilic syndrome was also established. This case represented a diagnostic challenge in the search for the definitive cause of the tricuspid stenosis.
References
- Gaasch WH. Tricuspid stenosis. UpToDate 2017.
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- Agarwala BN, Hijazi Z, Dearani J. Ebstein’s anomaly of the tricuspid valve. UpToDate 2011.
- Cogswell R, Schiller NB, Acquatella H. Endomyocardial fibrosis. UpToDate 2016.
- Calenda BW, Sergie Z, Love B, Larocca G, Naib T. Endomyocardial fibrosis due to hypereosinophilic syndrome mimicking Ebstein’s anomaly. J Am Coll Cardiol 2016;67:1186.
- Roufosse F, Klion AD, Weller PF. Hypereosinophilic syndromes: clinical manifestations, pathophysiology, and diagnosis. UpToDate 2017.
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Published:
2018-02-16
Issue:
Vol. 5 No. 4 (2018)
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