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Medullary Thyroid Carcinoma: Ethical Issues for the Surgeon

  • Healthcare Policy and Outcomes
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Abstract

Medullary thyroid cancer is a disease with an established genetic inheritance pattern for which evidence-based guidelines recommend genetic testing and subsequent management of affected patients and their family members. The perceived stigma of genetic testing, coupled with issues involving confidentiality and disclosure, create potential conflict and confusion. In some cases, there is a need for genetic testing and prophylactic surgery in children, augmenting the need for a judicious approach that balances respect for individual autonomy and parental rights with the best interest of the child. We provide an overview of the ethical issues facing surgeons caring for patients with familial medullary thyroid carcinoma, and recommend interventions and resources to assist in decision making in these difficult situations.

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Acknowledgment

The authors thank Mark E. Robson, MD, director of the Clinical Genetics Service, Memorial Sloan-Kettering Cancer Center, for his expert review.

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Authors and Affiliations

  1. Department of Surgery, Head and Neck Service, Memorial Sloan-Kettering Cancer Center, New York, NY, USA

    Andrew G. Shuman MD, Ashok R. Shaha MD & Luc G. T. Morris MD

  2. Division of Medical Ethics, Weill Cornell Medical College, New York, NY, USA

    Andrew G. Shuman MD & Joseph J. Fins MD, FACP

  3. Department of Medicine, Endocrinology Service, Memorial Sloan-Kettering Cancer Center, New York, NY, USA

    R. Michael Tuttle MD

Authors
  1. Andrew G. Shuman MD
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  2. Ashok R. Shaha MD
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  3. R. Michael Tuttle MD
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  4. Joseph J. Fins MD, FACP
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  5. Luc G. T. Morris MD
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Correspondence to Andrew G. Shuman MD.

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Shuman, A.G., Shaha, A.R., Tuttle, R.M. et al. Medullary Thyroid Carcinoma: Ethical Issues for the Surgeon. Ann Surg Oncol 19, 2102–2107 (2012). https://doi.org/10.1245/s10434-012-2235-4

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  • DOI: https://doi.org/10.1245/s10434-012-2235-4

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