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Auditory rehabilitation in neurofibromatosis type 2: a case for cochlear implantation

Published online by Cambridge University Press:  29 June 2007

Robert H. Temple ,
Patrick R. Axon ,
Richard T. Ramsden ,
Nesil Keles ,
Kemal Deger  and
Emre Yücel
Robert H. Temple*
Affiliation:
Department of Otolaryngology, Manchester Royal Infirmary, Manchester, UK
Patrick R. Axon
Affiliation:
Department of Otolaryngology, Manchester Royal Infirmary, Manchester, UK
Richard T. Ramsden
Affiliation:
Department of Otolaryngology, Manchester Royal Infirmary, Manchester, UK
Nesil Keles
Affiliation:
Instanbul Faculty of Medicine, Department of Otolaryngology, Capa-Istanbul, 343900, Turkey.
Kemal Deger
Affiliation:
Instanbul Faculty of Medicine, Department of Otolaryngology, Capa-Istanbul, 343900, Turkey.
Emre Yücel
Affiliation:
Instanbul Faculty of Medicine, Department of Otolaryngology, Capa-Istanbul, 343900, Turkey.
*
Address for correspondence: Mr R. H. Temple, Department of Otolaryngology, Manchester Royal Infirmary, Oxford Road, Manchester M13 9WL. Fax: 0161 276 8511
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Abstract

Cochlear implantation has a limited but definite role in the rehabilitation of certain neurofibromatosis type 2 (NF2) patients. The presence of a dead ear either before, or after, tumour removal does not necessarily imply loss of function in the eighth nerve; in some instances the hearing loss will be cochlear. Promontory or round window electrical stimulation may help to identify those individuals with surviving eighth nerve function. In such patients multichannel cochlear implantation promises a better level of audition than the auditory brain stem implant. This paper highlights such a case and the management problems are discussed.

Keywords

Neurofibromatosis 2Cochlear implantationNeuroma, acoustic
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 113 , Issue 2 , February 1999 , pp. 161 - 163
Copyright
Copyright © JLO (1984) Limited 1999

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